Mitral valve prolapse is the most common cause of primary mitral regurgitation. Arrhythmic mitral valve prolapse is a special entity that is characterised by ventricular arrhythmia and increased risk for sudden cardiac death. We present a 48-year old patient that was referred to our Department of Cardiology for elective invasive coronary angiography because of significant number of premature ventricular contractions observed on 24h-ECG ambulatory monitoring. Echocardiography and cardiac MRI revealed signs of arrhythmic mitral valve prolapse.